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Publikationer som ChEBI hänvisar till för sapropterin dihydrochloride. Visa hela publikationsregistret

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Publications in the selection

13 hits

Bibliografisk träff 2012-01-08

Evolving patient selection and clinical benefit criteria for sapropterin dihydrochloride (Kuvan®) treatment of PKU patients.

Gordon P, Thomas JA, Suter R, Jurecki E.

Mol Genet Metab · research support, non-u.s. gov't; journal article · DOI 10.1016/j.ymgme.2011.12.023

Bibliografisk träff 2011-10-29

START, a double blind, placebo-controlled pharmacogenetic test of responsiveness to sapropterin dihydrochloride in phenylketonuria patients.

Utz JR, Lorentz CP, Markowitz D, Rudser KD, Diethelm-Okita B, Erickson D, Whitley CB.

Mol Genet Metab · randomized controlled trial; journal article · DOI 10.1016/j.ymgme.2011.10.014

Bibliografisk träff 2011-08-16

Up to date knowledge on different treatment strategies for phenylketonuria.

Bélanger-Quintana A, Burlina A, Harding CO, Muntau AC.

Mol Genet Metab · research-article; review; journal article · DOI 10.1016/j.ymgme.2011.08.009

Bibliografisk träff 2011-05-30

Bi-modal dose-dependent cardiac response to tetrahydrobiopterin in pressure-overload induced hypertrophy and heart failure.

Moens AL, Ketner EA, Takimoto E, Schmidt TS, O'Neill CA, Wolin MS, Alp NJ, Channon KM, Kass DA.

J Mol Cell Cardiol · research support, non-u.s. gov't; research-article; journal article; research support, n.i.h., extramural · DOI 10.1016/j.yjmcc.2011.05.017

Bibliografisk träff 2011-03-31

Safety of extended treatment with sapropterin dihydrochloride in patients with phenylketonuria: results of a phase 3b study.

Burton BK, Nowacka M, Hennermann JB, Lipson M, Grange DK, Chakrapani A, Trefz F, Dorenbaum A, Imperiale M, Kim SS, Fernhoff PM.

Mol Genet Metab · clinical trial, phase iii; research support, non-u.s. gov't; multicenter study; journal article · DOI 10.1016/j.ymgme.2011.03.020

Bibliografisk träff 2010-11-15

Safety of sapropterin dihydrochloride (6r-bh4) in patients with pulmonary hypertension.

Robbins IM, Hemnes AR, Gibbs JS, Christman BW, Howard L, Meehan S, Cabrita I, Gonzalez R, Oyler T, Zhao L, Du RH, Mendes LA, Wilkins MR.

Exp Lung Res · multicenter study; clinical trial, phase i; journal article · DOI 10.3109/01902148.2010.512972

Bibliografisk träff 2010-08-09

New era in treatment for phenylketonuria: Pharmacologic therapy with sapropterin dihydrochloride.

Harding CO.

Biologics · review-article; journal article · DOI 10.2147/btt.s3015

Bibliografisk träff 2010-08-01

Sapropterin dihydrochloride: a new drug and a new concept in the management of phenylketonuria.

Trefz FK, Belanger-Quintana A.

Drugs Today (Barc) · research support, non-u.s. gov't; review; journal article · DOI 10.1358/dot.2010.46.8.1509557

Bibliografisk träff 2010-07-27

Activation of phenylalanine hydroxylase induces positive cooperativity toward the natural cofactor.

Gersting SW, Staudigl M, Truger MS, Messing DD, Danecka MK, Sommerhoff CP, Kemter KF, Muntau AC.

J Biol Chem · research support, non-u.s. gov't; research-article; journal article · DOI 10.1074/jbc.m110.124016

Bibliografisk träff 2010-06-16

Sapropterin dihydrochloride for phenylketonuria.

Somaraju UR, Merrin M.

Cochrane Database Syst Rev · systematic review; journal article · DOI 10.1002/14651858.cd008005.pub2

Bibliografisk träff 2010-04-03

Introduction of sapropterin dihydrochloride as standard of care in patients with phenylketonuria.

Vernon HJ, Koerner CB, Johnson MR, Bergner A, Hamosh A.

Mol Genet Metab · clinical trial; research-article; journal article; research support, n.i.h., extramural · DOI 10.1016/j.ymgme.2010.03.022

Bibliografisk träff 2010-02-23

Pahenu1 is a mouse model for tetrahydrobiopterin-responsive phenylalanine hydroxylase deficiency and promotes analysis of the pharmacological chaperone mechanism in vivo.

Gersting SW, Lagler FB, Eichinger A, Kemter KF, Danecka MK, Messing DD, Staudigl M, Domdey KA, Zsifkovits C, Fingerhut R, Glossmann H, Roscher AA, Muntau AC.

Hum Mol Genet · journal article · DOI 10.1093/hmg/ddq085

Bibliografisk träff 2010-02-01

Relative bioavailability of sapropterin from intact and dissolved sapropterin dihydrochloride tablets and the effects of food: a randomized, open-label, crossover study in healthy adults.

Musson DG, Kramer WG, Foehr ED, Bieberdorf FA, Hornfeldt CS, Kim SS, Dorenbaum A.

Clin Ther · comparative study; research support, non-u.s. gov't; randomized controlled trial; journal article · DOI 10.1016/j.clinthera.2010.02.012